Page 110 - Revista Portuguesa - SPORL - Vol 39. Nº2
P. 110
CARLOS VIDAl RLDONDO, PRANCISÇO ()LIVURA, lUIS MG IRE l! 54
MANUEL CUNHA, A. ()AMURO DOS SANÍOS
lendo ganho rclcvo nos últimos anos a linfomas cunl'nrmc u tipu celular -B ou 'l'- c
(Ilassmcução conjunta Europeia c Americana tendo em coma a provável a)rrcspnmléncia
-RliAl;. (Quadro 1) lista clnssilicnçãu divide os com n limbcilu normal que Ihc dá origem.
Quadro 1
Rlz‘AI. classijh‘ulirm (lc I..\'ll
Proposedmallgnancygrndaofmmasmed noordlngmoanBALclusmauon
mm mam
1. Indolent lymphoma (low-flak) l. Indolent lymphomas (low-rlsk)
Chronic lymphocytic leukaemia (CLL)/small Lug: granular lymphocytic leukaemia. T- and NK—
Lymphocyuc lymphoma cell types
Lymphoplasmacytic lymphoma/lmmunocytoma/ Mycosis fungoidcs (MP)
Waldcnsuõms macroglobulinzemia Smouldcflng and chronic adult T-ccll
Lcukacmia/lymphoma
Hairy-ccll leukaemia (HCL). including variant type (HTVL-l-positivc)
Splcnlc marginal-zonc lymphoma Cutaneous anaplastic largc-ccll lymphoma (ALCL)
Maxginal-zona B-ccll lymphoma:
Extranodal (MALT Bccll lymphoma. Iow-gradc)
Nodal (monocytoid)
Folliclc-ccntm lymphoma/follicular (small-ccll)
- grade I
Folliclc-ccmrc lymphoma/follimlar(mined small- And
larpcccll)
- grade [I
II. Aggressive lymphoma (intemedine—rlsk) ll. Agressive lymphoma (lntemldatc—rlsk)
Prolymphocytic leukaemia (PLL) Sémry's syndrome
Plasmacytoma/multiple mycloma Prolymphocytic leukaemia (PLL)
Mantlc-ccll lymphoma (MCL) Peripheral T-ccll lymphoma. unspecified
Folliclc-ccmcr lymphoma/follicular (largc-ccll) Angioimmunoblasuc lymphoma (AIL)
— grade lll Nasal type T/NK (angioccntric) lymphoma
Diffuse largc-B-ccll lymphoma (DLCL) (Including Intestinal T-ccll lymphoma
lmmunoblastic and ccntroblastic lymphoma and Non-cutancus anaplastic largc-ccll lymphoma
B-anaplasuc, intravascmar. MALT-B-ccll lymphoma
High-gradc, T-chl/histlocytc-rich B-ccll lym-
lmmunodcficcncy-associatcd Iymphoprollfcmiw 'disrdcrs, including post-transplant. AlDSrclatcadau
phoma) Primary mcdiastlnal (thymic) large-B—ccll
m. Very aggressive lymphoma (hIgh-risk)
lymphºmª
m. Very aggressive lymphoma (hIgh-dsk)
Precurso-B—lymphoblasnc lymphoma/lcukacmia Precursor T-lymphoblastlc lymphoma/lcukacmia
Adult T-ccll lymphoma/Icukacmia(A11J.). acute type
Burkitt 's lymphoma/B-ccll acute leukaemia
Plasma-ccll leukaemia (PCL)
mmm
primary immunodcflccncy-rclated lymphoma
220

