Page 110 - Revista Portuguesa - SPORL - Vol 39. Nº2
P. 110

CARLOS VIDAl RLDONDO, PRANCISÇO ()LIVURA, lUIS MG IRE l! 54
       MANUEL CUNHA, A. ()AMURO DOS SANÍOS





       lendo ganho rclcvo nos últimos anos a              linfomas cunl'nrmc u tipu celular -B ou 'l'- c
       (Ilassmcução conjunta Europeia c Americana         tendo em coma a provável a)rrcspnmléncia
       -RliAl;. (Quadro 1) lista clnssilicnçãu divide os  com n limbcilu normal que Ihc dá origem.

                                                   Quadro 1
                                           Rlz‘AI. classijh‘ulirm (lc I..\'ll

        Proposedmallgnancygrndaofmmasmed noordlngmoanBALclusmauon

        mm                                               mam

        1. Indolent lymphoma (low-flak)                   l. Indolent lymphomas (low-rlsk)
        Chronic lymphocytic leukaemia (CLL)/small        Lug: granular lymphocytic leukaemia. T- and NK—
        Lymphocyuc lymphoma                                cell types
        Lymphoplasmacytic lymphoma/lmmunocytoma/         Mycosis fungoidcs (MP)
        Waldcnsuõms macroglobulinzemia                   Smouldcflng and chronic adult T-ccll
                                                         Lcukacmia/lymphoma
        Hairy-ccll leukaemia (HCL). including variant type (HTVL-l-positivc)
           Splcnlc marginal-zonc lymphoma                Cutaneous anaplastic largc-ccll lymphoma (ALCL)
        Maxginal-zona B-ccll lymphoma:
        Extranodal (MALT Bccll lymphoma. Iow-gradc)
        Nodal (monocytoid)
        Folliclc-ccntm lymphoma/follicular (small-ccll)
        - grade I
        Folliclc-ccmrc lymphoma/follimlar(mined small- And
           larpcccll)
         - grade [I

        II. Aggressive lymphoma (intemedine—rlsk)        ll. Agressive lymphoma (lntemldatc—rlsk)
        Prolymphocytic leukaemia (PLL)                   Sémry's syndrome
         Plasmacytoma/multiple mycloma                   Prolymphocytic leukaemia (PLL)
         Mantlc-ccll lymphoma (MCL)                      Peripheral T-ccll lymphoma. unspecified
         Folliclc-ccmcr lymphoma/follicular (largc-ccll)  Angioimmunoblasuc lymphoma (AIL)
         — grade lll                                     Nasal type T/NK (angioccntric) lymphoma
         Diffuse largc-B-ccll lymphoma (DLCL) (Including Intestinal T-ccll lymphoma
           lmmunoblastic and ccntroblastic lymphoma and Non-cutancus anaplastic largc-ccll lymphoma
           B-anaplasuc, intravascmar. MALT-B-ccll lymphoma
           High-gradc, T-chl/histlocytc-rich B-ccll lym-
            lmmunodcficcncy-associatcd Iymphoprollfcmiw 'disrdcrs, including post-transplant. AlDSrclatcadau
           phoma) Primary mcdiastlnal (thymic) large-B—ccll
                                                         m. Very aggressive lymphoma (hIgh-risk)
           lymphºmª
         m. Very aggressive lymphoma (hIgh-dsk)
         Precurso-B—lymphoblasnc lymphoma/lcukacmia Precursor T-lymphoblastlc lymphoma/lcukacmia
                                                         Adult T-ccll lymphoma/Icukacmia(A11J.). acute type
            Burkitt 's lymphoma/B-ccll acute leukaemia
         Plasma-ccll leukaemia (PCL)
            mmm


         primary immunodcflccncy-rclated lymphoma

              220
   105   106   107   108   109   110   111   112   113   114   115