Page 77 - Revista Portuguesa - SPORL - Vol 41. Nº2

Rev. Pon. ORL. n.º4l. n.“ 2, ................ , Junho 2003

CASO CLÍNICO

LIPOSARCQMA DE HIPOFARINGE:

A PROPÓSITO DE UM CASO.
HYPOPHARYNGEAL LIPOSARCOMA: REPORT OF A CASE.

Beatriz Arenoz Búo', José Antonio Brandoriz Castelo”, Joaquin De Vergas Gutierrez*, Esther Conde Gallego“, Juan José Alvarez Vtcent””.

RESUMO:
Os lipasarcomas primários do laringe e hipoloringe são tumores extraordinariamente intrequentes. Na literature estéo descritos menos de 50 casos; a
maior parte incluem-se no gm 0 dos bem diferenciados. Os liposarcomas indilerenciados detinem-se coma liposarcomas bifésicos, com areas bem diferen-
ciadas e areas de células tusi ormes de alto grau, com pleomorfismo, atipia e elevado número de mitoses.
Propomos um tratamento conservador e assim mesmo reolizómos uma revisão da literatura com especial enlése no tratamento e prognóstico deste tipo
de tumores.
PALAVRAS CHAVE:
Liposarcoma, Hipotaringe, Laringe, Desditerenciado.
RESUMEN:
Los liposarcomas primarios de laringe e hipotaringe, son rumores extraordinariomente intrecuentes, en la literature hay descritos menos de 50 casos; la
mayor parte de ellos se incluyen dentro del grupo de los bien diferenciados. Los liposarcomas desditerenciados se detinen como liposorcomos bien diferen-
ciados con areas de células fusiformes de alto grado, con pleomorfismo, atipia y elevado número de mitosis.
Proponemos un tratamiento conservador, y asimismo realizamos una revisión de lo literature con especial éntasis en el tratamiento y pronéstico de este
tipo de tumores.
PALABRAS CLAVE:
Liposarcomo, Hipoforinge, laringe, Desdilerenciado.
SUMMARY:
Primary liposarcomas of the larynx and hypopharynx are extraordinarily rare tumors, with fewer than 50 cases identified in the available literature. Most
of them belong to welldifierentiated type, deditterentiated liposarcomo are defined as welldiflerentiated liposarcoma with areas of highgrade spindle cell
non»lipogenic sarcoma.
We present a case of dedifferenlioted liposarcoma arising from the hypopharyx, we propose a conservative treatment and review of the literature with
special emphasis on treatment and prognosis of this kind of tumor.
KEY WORDS:
Liposarcoma, Hypopharynx, Lorynx, DediHerentiated.

INTRODUCTION liposarcomas“, and they often originate in the
soft tissues of the neck. Primary liposarcomas of
Liposarcoma is the second most common soft the larynx and hypopharynx are exceedingly
tissue sarcoma in the adult population, account- rare, the first case was reported by Miller et al in
ing for approximately 15% of all sarcomas. It is 19758. Fewer than 50 cases have been identified
most commonly found in the lower extremities in the available literature5 ‘5, most of them belong
and the retroperitoneum. The incidence in the to well-diFlerentiated type. We present a case of
head and neck is between 3% and 8% of all deditferentiated liposarcoma in the hypopharyx.

Medical staff at Otolaryngolongeod & Neck Surgery Department, University Hospital "Doce de Octubre”, Madrid
Medical sic“ at Otolaryngology-Head & Neck Surgery Department, University Hospltal "Doce de Octubve", Madrid and assooate professor of O'olaryngology ov
Complutense University of Madrid
' ' ' Resident at Pathology Department, University Hospital "Doce de Octubre", Modnd
....
Chief ol OtolaryngologyAHeod & Neck Surgery Department University Hospital "Doce de Octubre", Madnd and Professor of Otolaryngology ov Compíuvense Unwerstty
ot Madrid
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